干旱区生态环境知识资源中心(Arid): Short QT syndrome: The current evidences of diagnosis and management

Arid

DOI	10.1002/joa3.12439
	Short QT syndrome: The current evidences of diagnosis and management
	Dewi, Ivana P.; Dharmadjati, Budi B.
通讯作者	Dewi, IP
来源期刊	JOURNAL OF ARRHYTHMIA
ISSN	1880-4276
EISSN	1883-2148
出版年	2020
卷号	36 期号:6 页码:962-966
英文摘要	There are many cardiac arrhythmias and sudden cardiac death (SCD) related to channelopathies or ion channel disorders. Short QT syndrome (SQTS) is an inherited cardiac channelopathy principally caused by defective functioning of both potassium-calcium ion channel that lead to abnormal shortening of QT interval, and an increased risk of ventricular and atrial arrhythmias. Tall T waves in all lead electrocardiogram (ECG), peaked T waves, and narrow-based T waves that are reminiscent of the typical "desert tent" T waves of hyperkalemia are frequently associated with SQTS. Diagnosis is based on patient's family history, evaluation of symptoms (palpitations and cardiac arrest), and 12-lead ECG. It can be time challenging because of the wide range of QT interval in healthy subjects. Implantable cardioverter defibrillator (ICD) is the first-line therapy in SQTS. Quinidine has the potential to be an effective pharmacological therapy for SQTS patients, especially in young children who are not feasible in ICD implantation, because of the ability to prolong QT interval.
英文关键词	channelopathies short QT syndrome sudden cardiac death
类型	Review
语种	英语
开放获取类型	DOAJ Gold, Green Published
收录类别	ESCI
WOS记录号	WOS:000575303000001
WOS关键词	SUDDEN CARDIAC DEATH ; PREVALENCE ; INTERVALS ; MUTATION ; REPOLARIZATION ; QUINIDINE ; RISK ; LONG
WOS类目	Cardiac & Cardiovascular Systems
WOS研究方向	Cardiovascular System & Cardiology
资源类型	期刊论文
条目标识符	http://119.78.100.177/qdio/handle/2XILL650/334635
作者单位	[Dewi, Ivana P.; Dharmadjati, Budi B.] Univ Airlangga, Fac Med, Surabaya, Indonesia; [Dewi, Ivana P.] Duta Wacana Christian Univ, Fac Med, Yogyakarta, Indonesia; [Dewi, Ivana P.; Dharmadjati, Budi B.] Dr Soetomo Gen Hosp, Dept Cardiol & Vasc Med, Surabaya, Indonesia
推荐引用方式 GB/T 7714	Dewi, Ivana P.,Dharmadjati, Budi B.. Short QT syndrome: The current evidences of diagnosis and management[J],2020,36(6):962-966.
APA	Dewi, Ivana P.,&Dharmadjati, Budi B..(2020).Short QT syndrome: The current evidences of diagnosis and management.JOURNAL OF ARRHYTHMIA,36(6),962-966.
MLA	Dewi, Ivana P.,et al."Short QT syndrome: The current evidences of diagnosis and management".JOURNAL OF ARRHYTHMIA 36.6(2020):962-966.