干旱区生态环境知识资源中心(Arid): BuddChiari综合征血管病变的分型与临床研究

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	BuddChiari综合征血管病变的分型与临床研究
其他题名	Clinical study and reclassification of the vascular lesion in patients with Budd-Chiari syndrome
	徐克 1; 有慧 1; 苏洪英 1; 祖茂衡 2; 赵金旭 3; 崔进国 4; 杨学良 5
来源期刊	中华放射学杂志
ISSN	1005-1201
出版年	2003
卷号	37 期号:10 页码:896-900
中文摘要	目的探讨Budd-Chiari综合征(BCS)的病变特点及合理分型。方法对来自5个BCS高发地区并按统一方案确诊的412例BCS患者的血管造影等影像学检查结果及临床资料进行统计学分析。结果将BCS分为单纯肝静脉病变(Ⅰ型)、下腔静脉(IVC)膜性病变(Ⅱ型)、IVC膜性病变伴远端腔内血栓形成(Ⅲ型)和IVC节段性病变(Ⅳ型)4种类型，并将Ⅰ型分为局限型和弥漫型，将Ⅱ～Ⅳ型各分为伴有和不伴有1支以上肝静脉开放的8种亚型。根据该方案分型：I型49例，占11.9%；Ⅱ型208例，占50.5%；Ⅲ型19例，占4.6%；Ⅳ型136例，占33.0%。4组患者间平均发病年龄无显著性意义(F=1.63，P>0.05)。但平均病程有明显不同：I型短于其他3型(P<0.05)；Ⅳ型长于Ⅱ型(q=4.33，P<0.05)和I型(q=6.36，P<0.05)；而Ⅱa与Ⅱb及Ⅳa与Ⅳb型之间的平均病程比较无显著性意义(P>0.05)。结论 (1)伴有1支或1支以上肝静脉开放的IVC膜性阻塞性病变(Ⅱa型)是该组BCS的主要类型。(2)BCS血管病变的各种类型考虑是一由狭窄到闭塞、由膜性向节段性病变逐渐发展演化的过程，尤其是Ⅱ型、Ⅲ型和Ⅳ型病变是整个疾病进展过程中具有因果关系的不同阶段。(3)再分型方案对BCS治疗方法的选择和预后的评价具有指导意义。
英文摘要	Objective To assess the features and rational reclassification of the vascular lesion in patients with Budd-Chiari syndrome (BCS) in China. Method Four hundred and twelve BCS patients were included in this study, and the patients were diagnosed by consolidated scheme from 5 provinces of China, where high incidence of BCS was reported. The results of image examination, such aa vascular angiography and related clinical data were statistically analyzed. Results A new classification scheme for BCS was presented: simple hepatic vein lesion (type I ) , membranous obstruction of the inferior vena cava (type II ) , membranous obstruction of the inferior vena cava with thrombosis in the distant lumen (type III) , and segmental obstruction of the inferior vena cava (type IV). Type I was subdivided into two types ? local and diffuse subtype. According to the situation whether there was opening hepatic vein or not, type H lo type IV was each subdivided into two subtypes. According to the above-mentioned classification scheme, the patients in our series could be divided into four groups; 49 oases of type I (11. 9% ) , 208 cases of type II (50. 5% ), 19 cases of type I (4. 6% ), and 136 cases of type IV (33. 0% ). There was no statistical difference among the mean onset ages for the four groups (F = 1.63, P>0.05). The mean duration of the disease in type I was significantly shorter than that in the other three types. The mean course of the disease of type IV was longer than that of type I (q=4.33, P <0. 05) and type I ((7 = 6. 36,P < 0. 05). There was no significant difference in the mean duration of the disease between type E a and II b (t = 0. 872, P > 0,05), as well as between IV a and IV b (t = 0. 599, P > 0. 05). Conclusion (1) Membranous obstruction of IVC with one or more opening hepatic veins (Ha) is the main type of BCS in China. (2) The formation of BCS lesion with inferior vena cava is a developing course. Type II , type US., and type IV are the different stages of the developing course. (3) The reclassification scheme has directive significance in selecting more suitable therapy method of the BCS.
中文关键词	肝静脉血栓形成 ; 肝静脉闭塞性疾病 ; 血管造影术 ; 数字减影
英文关键词	hepatic vein thrombosis hepatic veno-occlusive disease angiography, digital subtraction
语种	中文
国家	中国
收录类别	CSCD
WOS类目	MEDICINE GENERAL INTERNAL
WOS研究方向	General & Internal Medicine
CSCD记录号	CSCD:1263468
资源类型	期刊论文
条目标识符	http://119.78.100.177/qdio/handle/2XILL650/204718
作者单位	1.中国医科大学附属第一医院放射科, 沈阳, 辽宁 110001, 中国; 2.徐州医学院附属医院介入放射科; 3.山东省菏泽地区人民医院介入科; 4.解放军白求恩国际和平医院放射科; 5.解放军第一五○医院放射科
推荐引用方式 GB/T 7714	徐克,有慧,苏洪英,等. BuddChiari综合征血管病变的分型与临床研究[J],2003,37(10):896-900.
APA	徐克.,有慧.,苏洪英.,祖茂衡.,赵金旭.,...&杨学良.(2003).BuddChiari综合征血管病变的分型与临床研究.中华放射学杂志,37(10),896-900.
MLA	徐克,et al."BuddChiari综合征血管病变的分型与临床研究".中华放射学杂志 37.10(2003):896-900.